HEMOPHILIA

Course overview

HEMOPHILIA A AND B ARE THE MOST COMMON SEVERE HEREDITARY HEMORRHAGIC DISORDERS. HEMOPHILIA A AND B RESULT FROM FACTOR VIII AND FACTOR IX PROTEIN DEFICIENCY. PATIENTS PRESENT WITH PROLONGED BLEEDING WITH OR WITHOUT TRAUMA, DEPENDING ON THE FACTOR ACTIVITY. THE PRINCIPAL AIM OF CARE SHOULD BE TO AVOID AND TREAT BLEEDING. THE PATIENT SHOULD RECEIVE TREATMENT IN A COMPREHENSIVE TREATMENT CENTER WHERE INTERPROFESSIONAL SERVICES ARE OFFERED AT ALL TIMES TO THE PATIENTS AND THEIR FAMILIES. THIS ACTIVITY REVIEWS THE EPIDEMIOLOGY, NATURAL HISTORY, EVALUATION, AND MANAGEMENT OF HEMOPHILIA AND ALSO HIGHLIGHTS THE ROLE OF THE INTERPROFESSIONAL TEAM IN EVALUATING, MANAGING, AND IMPROVING CARE FOR PATIENTS WITH THIS CONDITION.