VON HIPPEL-LINDAU SYNDROME

Course overview

Von Hippel-Lindau syndrome (VHL) is a rare inherited disorder characterized by the development of cysts and benign and malignant tumors in various organs and systems, including the central nervous system (CNS), retina, kidneys, and endocrine glands. The most common neoplasms in patients with VHL are hemangioblastomas, vascular tumors of the posterior cranial fossa, spinal cord, and retina, which although slow growing and histologically benign are associated with high morbidity and mortality due to their localization and high risk of hemorrhage. This continuing education module is designed to give the reader/learner an increased understanding of VHL, its clinical presentation, symptoms, and treatment, and to aid in caring for the patient with this diagnosis. Readers may explore any or all of the topics. One contact hour of continuing education credit is available for those who successfully complete the post-test and evaluation form.