SUPRAVALVAR AORTIC STENOSIS

Course overview

SUPRAVALVULAR AORTIC STENOSIS (SVAS) IS A CONGENITAL HEART DEFECT THAT ACCOUNTS FOR 8 TO 14 PERCENT OF ALL CASES OF CONGENITAL AORTIC STENOSIS. IT INVOLVES A NARROWING OF THE PORTION OF THE AORTA LOCATED JUST ABOVE THE AORTIC VALVE. THE THREE TYPES OF SVAS THAT HAVE BEEN RECOGNIZED ARE HOURGLASS, MEMBRANOUS, AND HYPOPLASIA OF THE AORTIC ARCH. THIS ACTIVITY DESCRIBES THE EVALUATION, DIAGNOSIS, AND MANAGEMENT OF SUPRAVALVULAR AORTIC STENOSIS AND HIGHLIGHTS THE ROLE OF TEAM-BASED INTERPROFESSIONAL CARE FOR AFFECTED PATIENTS.