TURCOT SYNDROME
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TURCOT SYNDROME IS THE ASSOCIATION OF PRIMARY BRAIN TUMORS WITH COLORECTAL CANCER. HEREDITARY NON-POLYPOSIS COLORECTAL CANCER (HNPCC) AND FAMILIAL ADENOMATOUS POLYPOSIS (FAP) ARE THE 2 MOST WELL-KNOWN INHERITED COLORECTAL CANCERS. IF A BRAIN TUMOR ARISES IN A PATIENT WITH EITHER HNPCC OR FAP, THEN THE PATIENT IS CONSIDERED TO HAVE TURCOT SYNDROME 1 (TS1) OR TURCOT SYNDROME 2 (TS2). THIS ACTIVITY REVIEWS THE EVALUATION AND MANAGEMENT OF TURCOT SYNDROME AND HIGHLIGHTS THE ROLE OF INTERPROFESSIONAL TEAM MEMBERS IN COLLABORATING TO PROVIDE WELL-COORDINATED CARE AND ENHANCE OUTCOMES FOR AFFECTED PATIENTS.
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