PULMONARY IDIOPATHIC HYPERTENSION

Course overview

PULMONARY HYPERTENSION (PH) IS DEFINED AS MEAN PULMONARY ARTERY PRESSURE GREATER THAN 25 MM HG MEASURED DURING RIGHT HEART CATHETERIZATION. THE TERM PULMONARY ARTERY HYPERTENSION (PAH) DESCRIBES A SUBSET OF PATIENTS WHO ALSO HAVE THE PRESENCE OF PRE-CAPILLARY HYPERTENSION INCLUDING AN END-EXPIRATORY PULMONARY ARTERY WEDGE PRESSURE (LESS THAN 15 MM HG) AND A PULMONARY VASCULAR RESISTANCE GREATER THAN 3 WOODS UNITS. THIS ACTIVITY WILL FOCUS ON IDIOPATHIC PULMONARY ARTERY HYPERTENSION (IPAH), WHICH CORRESPONDS TO SPORADIC DISEASE, IN THE ABSENCE OF FAMILY HISTORY AND HIGHLIGHT THE ROLE OF THE INTERPROFESSIONAL TEAM IN ITS MANAGEMENT.