LAUGIER-HUNZIKER SYNDROME

Course overview

LAUGIER-HUNZIKER SYNDROME, ALSO KNOWN AS LAUGIER-GERBIG-HUNZIKER SYNDROME OR LAUGIER-HUNZIKER-BARAN SYNDROME OR IDIOPATHIC LENTICULAR MUCOCUTANEOUS PIGMENTATION, IS A HEREDITARY PIGMENTARY DISORDER CHARACTERIZED BY A UNIQUE EXPRESSION OF PIGMENTATION OVER THE MUCOSAL, NAIL, AND ACRAL SITES. IT IS COMMONLY MISTAKEN FOR ADDISON'S DISEASE, PEUTZ JEGHERS SYNDROME, CRONKHITE-CANADA SYNDROME. THE CONDITION IS KNOWN TO BE BENIGN NEVERTHELESS A FEW ASSOCIATIONS WITH ESOPHAGEAL MELANOCYTOSIS, ACTINIC LICHEN PLANUS, HYPOCELLULAR BONE MARROW, AND THROMBOCYTOPENIA HAVE BEEN REPORTED. THIS ACTIVITY PRESENTS THE CLINICAL PRESENTATION, EVALUATION, AND MANAGEMENT OF LAUGIER-HUNZIKER SYNDROME AND HIGHLIGHTS THE ROLE OF THE INTERPROFESSIONAL TEAM IN THE MANAGEMENT OF AFFECTED PATIENTS.