EBSTEIN ANOMALY AND MALFORMATION

Course overview

EBSTEIN ANOMALY OF THE TRICUSPID VALVE IS A CONGENITAL MALFORMATION, IN WHICH THERE IS DOWNWARD DISPLACEMENT OF INSERTION OF SEPTAL AND POSTERIOR LEAFLETS. ANTERIOR LEAFLET IS NOT USUALLY AFFECTED. THE TRICUSPID VALVE LEAFLETS ARE DYSPLASTIC. AS A RESULT OF THE DISPLACEMENT, THERE IS POOR COAPTATION OF THE VALVE LEAFLETS LEADING TO TRICUSPID REGURGITATION, WHICH IN TURN CAUSES RIGHT ATRIAL ENLARGEMENT OF A VARIABLE DEGREE DEPENDING UPON THE DEGREE OF TRICUSPID REGURGITATION. THIS ACTIVITY REVIEWS THE PATHOPHYSIOLOGY AND PRESENTATION OF EBSTEIN ANOMALY AND HIGHLIGHTS THE ROLE OF THE INTERPROFESSIONAL TEAM IN ITS MANAGEMENT.