LYMPHOMATOID PAPULOSIS

Course overview

LYMPHOMATOID PAPULOSIS IS A NON-AGGRESSIVE T-CELL LYMPHOMA CHARACTERIZED BY RECURRENT, SPONTANEOUSLY-REGRESSIVE PAPULONODULAR AND SOMETIMES, NECROTIC LESIONS, OFTEN DISSEMINATED WITH HISTOLOGIC FEATURES SUGGESTIVE OF A CD30-POSITIVE LYMPHOMA. IT ACCOUNTS FOR ABOUT 12% OF CUTANEOUS LYMPHOMAS. IT IS CLASSIFIED, ALONGSIDE PRIMARY CUTANEOUS ANAPLASTIC LARGE CELL LYMPHOMA, IN THE GROUP OF T-CELL PROLIFERATIONS EXPRESSING CD30. PATIENTS AFFECTED WITH LYMPHOMATOID PAPULOSIS ARE AT RISK OF DEVELOPING ANOTHER HEMATOLOGICAL DISORDER: MAINLY MYCOSIS FUNGOIDES, ERYTHRODERMIC T-CELL LYMPHOMA, HODGKIN DISEASE OR LARGE-CELL CD30+ LYMPHOMA. THIS ACTIVITY REVIEWS THE EVALUATION AND TREATMENT OF LYMPHOMATOID PAPULOSIS AND HIGHLIGHTS THE ROLE OF THE INTERPROFESSIONAL TEAM IN EVALUATING AND TREATING THIS CONDITION.