CONGENITAL NEPHROTIC SYNDROME

Course overview

CONGENITAL NEPHROTIC SYNDROME (CNS) IS DEFINED WHEN IT PRESENTS WITHIN THREE MONTHS OF BIRTH. IT CONSISTS OF HEAVY PROTEINURIA, EDEMA, HYPOALBUMINEMIA, HYPOGAMMAGLOBULINEMIA, HYPERCOAGULABILITY, AND HYPERLIPIDEMIA. MANAGEMENT IS VERY CHALLENGING AS PATIENTS ARE PRONE TO COMPLICATIONS SUCH AS INFECTION, THROMBOSIS, AND FAILURE TO THRIVE. THIS ACTIVITY OUTLINES THE EVALUATION AND TREATMENT OF CONGENITAL NEPHROTIC SYNDROME AND EMPHASIZES THE ROLE OF THE INTERPROFESSIONAL TEAM IN THE CARE OF PATIENTS WITH THIS CONDITION.