BLUE RUBBER BLEB NEVUS SYNDROME
Tracking # 20-1046908
$99999.00
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BLUE RUBBER BLEB NEVUS SYNDROME IS ALSO KNOWN AS BEAN SYNDROME. IT IS A RARE SYNDROME OF VENOUS MALFORMATIONS THAT ARISE IN THE SKIN AND GASTROINTESTINAL TRACT. PATIENTS PRESENT WITH MULTIPLE VENOUS MALFORMATIONS IN VARIOUS ORGAN SYSTEMS INCLUDING THE LIVER, SPLEEN, HEART, EYE, AND CENTRAL NERVOUS SYSTEM. PATIENTS WITH BLUE RUBBER BLEB NEVUS SYNDROME ARE AT INCREASED RISK FOR GASTROINTESTINAL HEMORRHAGE AND SEVERE IRON DEFICIENCY ANEMIA. THIS ACTIVITY REVIEWS THE EVALUATION AND MANAGEMENT OF BLUE RUBBER BLEB NEVUS SYNDROME AND HIGHLIGHTS THE ROLE OF THE INTERPROFESSIONAL TEAM IN IMPROVING CARE FOR PATIENTS WITH THIS CONDITION.
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